MedSchool: Ace Your OSCEsThe Medical Company
GET - On the App Store
ECG Disease Patterns
ECG Disease Patterns

Congenital Long QT Syndrome

February 15th, 2021


Several hereditary conditions are associated with a prolonged QT interval, which increases the risk of life-threatening arrhythmia.
A prolonged QT interval represent delayed ventricular repolarisation, and increases the risk of a re-entry circuit from froming (i.e. Torsade de Pointes).
  • Congenital Long QT Syndromes

  • Romano-ward syndrome (LQT1-6) - isolated prolonged QT precipitated by various triggers
  • Jervell and Lange-Nielsen syndrome (JLNS)
  • Anderson-Tawil syndrome (LQT7) - prolonged QT, periodic paralysis, facial abnormalities
  • Timothy syndrome (LQT8) - prolonged QT, AV block, congenital heart disease, developmental delay, dysmorphic features
ECG MorphologyBroad T wavesBifid T wavesLate T waves
TriggerExertion, fright, swimmingAuditorySleep / rest
Next Page
Want more info like this?
  • Your electronic clinical medicine handbook
  • Guides to help pass your exams
  • Tools every medical student needs
  • Quick diagrams to have the answers, fast
  • Quizzes to test your knowledge
Sign Up Now

Snapshot: Initialising...